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Pani i kēia pahu huli.

Nā loulou pono no ʻoe

Nā ʻano Lymphoma ʻē aʻe

Kaomi ma aneʻi e ʻike i nā ʻano lymphoma ʻē aʻe

T-cell Lymphoma

ʻO nā Lymphomas T-cell he pūʻulu ma kahi o 20 mau maʻi maʻi maʻi ʻokoʻa loa. Ma Australia, ma kahi o 450 wale nō ka poʻe i loaʻa i ka T-cell lymphoma i kēlā me kēia makahiki.

Hāʻawi kēia ʻaoʻao i kahi hiʻohiʻona o nā lymphomas T-cell, kahi hoʻomaka maikaʻi loa i ka wā i ʻike mua ʻia ai ʻoe me T-cell lymphoma. Hāʻawi ia i ka ʻike maʻamau a me nā loulou pono no ʻoe e aʻo ai e pili ana i ka lymphoma, nā lymphocytes T-cell, nā hōʻailona, ​​​​ka maʻi a me ke kau ʻana.

Inā ʻike ʻoe i kāu subtype o T-cell lymphoma, aia nā loulou i kēia mau mea ma lalo o kēia ʻaoʻao i hiki iā ʻoe ke loaʻa i nā ʻike kikoʻī e pili ana iā ʻoe. Inā ʻaʻole ʻoe maopopo i kāu ʻano subtype, e nīnau iā ʻoe i ke kauka loea.

I kēia ʻaoʻao:

He aha ka Lymphoma?

ʻO ka Lymphoma kahi huaʻōlelo i hoʻohana ʻia no kahi hui o nā maʻi ʻokoʻa he 80 e hoʻomaka ana i ka wā e lilo ai nā pūpū koko i kapa ʻia nā lymphocytes i ka maʻi kanesa. Loaʻa iā mākou nā ʻano lymphocytes ʻelua, ʻo ia nā lymphocytes B-cell a me nā lymphocytes T-cell.

ʻO nā lymphomas T-cell ka maʻi kanesa o nā lymphocytes T-cell, a ʻoi aku ka kakaikahi ma mua o nā lymphomas-cell. No ka hoʻomaopopo ʻana i nā lymphomas T-cell, pono ʻoe e ʻike mua i ka lymphoma. E ʻoluʻolu e ʻike i kā mākou He aha ka Lymphoma pūnaewele no ka ʻike ʻana i ka lymphoma.

No kaʻike hou aku
He aha ka lymphoma?

Ka hoʻomaopopo ʻana i nā Lymphocytes T-cell

He ʻāpana koʻikoʻi nā lymphocytes T-cell o kā mākou ʻōnaehana pale e pale iā mākou mai ka maʻi a me ka maʻi, a hoʻoponopono i kā mākou ʻōnaehana pale e pale aku i nā hōʻeha autoimmune. Hana ʻia ka hoʻouka kaua ʻana i ka wā ʻoi aku ka hana o kā mākou ʻōnaehana pale ʻole a hoʻomaka e hakakā i ko mākou kino ponoʻī ma mua o ka maʻi a me ka maʻi.

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ʻO kāu ʻōnaehana lymphatic kahi ʻāpana o kāu ʻōnaehana pale a mālama iā ʻoe i ke olakino ma ke kaua ʻana i nā germs. Loaʻa ia i kāu mau lymph nodes, nā moku lymphatic a me nā ʻāpana e like me kāu spleen, thymus a me nā mea ʻē aʻe. Noho nui kāu mau lymphocytes B-cell i kāu ʻōnaehana lymphatic.

E pili ana i nā Lymphocytes T-cell

  • Hana ʻia nā pūnae T i loko o ko mākou iwi iwi, ʻoʻo i loko o ko mākou thymus, akā hiki ke noho ma kekahi ʻāpana o kā mākou lymphatic system - me kā mākou lymph nodes.
  • Pono e ho'ā 'ia ka hapa nui o nā pūnaewele T no ka hana pono. Hoʻomaha maʻamau lākou i loko o kā mākou thymus a i ʻole nā ​​ʻāpana ʻē aʻe o kā mākou lymphatic system, a ala wale lākou a hakakā i ka maʻi i ka wā e hōʻike ai nā cell immune ʻē aʻe iā lākou he maʻi a maʻi paha e hakakā. I ko lākou ala ʻana, hiki i nā pūnae T ke hele i kekahi ʻāpana o ko mākou kino e hakakā i ka maʻi a i ʻole ka maʻi.
  • ʻO kekahi mau T-cell ke kuleana no ka "hoʻoponopono" i ka pane immune. ʻO ia hoʻi, ke luku ʻia kahi maʻi, ʻo ka “Nā pūnaewele T hoʻoponopono” e haʻi aku i nā pūnaewele ʻē aʻe e "kū i lalo" i ʻole lākou e hoʻomau i ka hakakā a hoʻopilikia i kā mākou mau sela maikaʻi.
  • Kāhea pinepine ʻia nā cell Killer Natural (NK). “Nā pūnaewele NK”. ʻO lākou nā pūnaewele immune kūikawā e ʻike a luku i nā maʻi kanesa. ʻAʻole e like me nā mea T-cell ʻē aʻe, ʻaʻole pono e hoʻāla ʻia nā cell NK e hakakā i ka maʻi kanesa. Mākaukau lākou e hakakā i nā manawa a pau, a neʻe ikaika a puni kou kino i ka nānā ʻana i nā cell i loaʻa nā loli maʻi maʻi.
  • Ma hope o ka hakakā ʻana i kahi maʻi a i ʻole maʻi, lilo kekahi mau T-cell “Memory T-cells”. Hoʻomanaʻo lākou i nā mea a pau e ʻike ai e pili ana i ka maʻi a pehea e hakakā ai. ʻO ia ala, inā loaʻa hou iā mākou ka maʻi like a i ʻole ka maʻi, hiki i kā mākou ʻōnaehana pale ʻana ke hakakā me ka wikiwiki a me ka maikaʻi.
  • Hiki i kekahi mau T-cell ke kōkua i nā mea ʻē aʻe, e like me nā lymphocytes B-cell e hana pono. Ua kapa ʻia kēia mau T-cell "Kōkua T-cell”.

He aha nā lymphoma T-cell?

ʻO nā lymphoma T-cell he ʻano o Non-Hodgkin Lymphoma (NHL) e ulu ana mai nā lymphocytes T-cell. He kakaikahi lākou, a ʻo ka hapa nui o nā lymphoma T-cell e ulu ana mai nā pūnae T oʻo. Hoʻopilikia pinepine kēia mau lymphoma T-cell i nā pākeke ma luna o 60 mau makahiki a ʻoi aku ka maʻamau i nā kāne ma mua o nā wahine.

Eia nō naʻe, i kekahi manawa hiki ke hoʻomohala ʻia ka lymphoma T-cell mai nā pūnae T oʻo ʻole. Kapa ʻia kēia ʻano lymphoblastic lymphoma a ʻoi aku ka maʻamau o kēia ʻano i nā keiki a me nā ʻōpio.

Nā kumu o ka T-cell lymphoma

ʻAʻole maopopo iā mākou ke kumu o ka T-cell lymphoma. Aia kekahi mau noiʻi e hōʻike ana i kekahi mau kumu e hoʻonui i kou pilikia o ka hoʻomohala ʻana i ka lymphoma, akā ʻo ka hapa nui o nā poʻe me kēia mau mea pilikia ʻaʻole e ulu i ka lymphoma. ʻO kekahi mau mea pilikia i ʻike ʻia:

  • Hoʻopili ʻia ka maʻi me ke kanaka T-lymphotropic virus type 1 (HTLV-1) me ka ulu ʻana o ka maʻi leukemia/lymphoma T-cell makua (ATLL).
  • Hoʻopili ʻia ka maʻi ma mua me ka maʻi Epstein-Barr (EBV) i ka hoʻomohala ʻana o nā ʻano lymphomas, me ka angioimmunoblastic T-cell lymphoma (AITL).
  • Hoʻopili ʻia ka T-cell lymphoma (EATL) pili i ka enteropathy me ka maʻi celiac.

No kaʻike hou aku
Nā kumu a me nā kumu pilikia o ka lymphoma

Nā hōʻailona o nā lymphomas T-cell

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Ma kahi o 20 mau ʻano like ʻole o T-cell lymphoma hiki ke hoʻomaka ma kekahi wahi o kou kino, ʻokoʻa loa nā hōʻailona ma waena o ka poʻe me T-cell lymphoma.

Aia kekahi mau hōʻailona maʻamau i nā poʻe he nui me ka lymphoma, a ʻo nā mea ʻē aʻe i kapa ʻia ʻo B-symptoms pono ʻoe e hōʻike koke i kāu kauka. Hōʻike ʻia kēia mau hōʻailona ma nā kiʻi ma lalo nei, akā no ka nānā hohonu ʻana i nā hōʻailona e kaomi i ka loulou ma lalo o nā kiʻi.

 

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No kaʻike hou aku
Nā ʻōuli o Lymphoma

ʻO ka hōʻoia a me ke kau ʻana o nā lymphomas T-cell

Hiki ke paʻakikī ke ʻike ʻana i nā lymphomas T-cell no ʻekolu kumu nui. Aia kēia mau mea:

  • hiki iā lākou ke hoʻomaka ma kekahi wahi o kou kino
  • nui nā hōʻailona like me nā mea i ʻike ʻia ma nā maʻi ʻē aʻe, a
  • Kakaʻikahi loa lākou no laila ka nui o nā kauka lapaʻau (GP) ʻaʻole i mālama i kekahi me ka T-cell lymphoma.

ʻO ka hana mua i ka loaʻa ʻana o kahi maʻi maʻi, ʻo ka loaʻa ʻana o kahi biopsy o ka pehu lymph node a i ʻole kekahi wahi o kou kino i hoʻopilikia ʻia. Hiki i kēia ke komo i kahi biopsy ʻili inā pili kāu lymphoma i kou ʻili.

 

ʻike,

E kau ma luna o kēia kāleka no ka ʻike hou aku
ʻO kahi hōʻailona ke ʻano o kou (lymphoma), a ʻo ia ka subtype.
Kaomi ma aneʻi e ʻike i nā ʻano ʻano o ka lymphoma

Ke hoʻonohonoho

E kau ma luna o kēia kāleka no ka ʻike hou aku
ʻO ka staging e pili ana i ka nui o ka lymphoma o kou kino i loko, a ma hea kahi lymphoma. ʻO ka pae mua a me ʻelua lymphomas i manaʻo ʻia i ka wā mua. Manaʻo ʻia ka pae ʻekolu a me ka pae ʻehā.
No ka ʻike hou aku e pili ana i ka hoʻokūkū e kaomi ma aneʻi

Kāleka

E kau ma luna o kēia kāleka no ka ʻike hou aku
ʻO ka helu ʻana e pili ana i ka wikiwiki o ka ulu ʻana o ka lymphoma a me ka ʻokoʻa o ke ʻano o nā pūnaewele lymphoma i hoʻohālikelike ʻia i kāu mau pūnaewele T maʻamau.

Pono paha ʻoe i nā hoʻāʻo

Pono paha ʻoe i nā ʻano hoʻāʻo like ʻole e loaʻa i ka maʻi T-cell lymphoma, e hana i kāu ʻano subtype, pae a me ka papa. E nānā i ke wikiō ma lalo nei e lohe ai mai ka Luna Hoʻokele Haematologist ʻo Dr Dejan Radeski e pili ana i nā hoʻokolohua āu e pono ai.

No ka ʻike hou aku e nānā
ʻO ka mea aʻoaʻo Haematologist ʻo Dr Dejan Radeski, e kamaʻilio e pili ana i nā lymphoma T-cell.

Pehea e mālama ʻia ai ka lymphoma T-cell?

ʻO ke ʻano o ka lapaʻau e pono ai ʻoe no ka T-cell lymphoma e hilinaʻi ʻia ma ke ʻano subtype o lymphoma, inā he palaualelo a ʻeha paha, kou mau hōʻailona a me kou makemake pilikino. Aia ma lalo kahi hiʻohiʻona o kekahi o nā ʻano lapaʻau e hāʻawi ʻia iā ʻoe. 

Radiotherapy no ka lymphoma
Hiki ke hoʻohana ʻia ka radiotherapy e mālama i ka lymphoma, a i ʻole e hoʻomaikaʻi i kāu mau hōʻailona

Hoʻohana ʻia ka radiotherapy i nā kukui uila kiʻekiʻe (radiation), e pepehi i nā maʻi maʻi maʻi. Hiki ke hoʻohana ʻia ma ke ʻano he lapaʻau iā ia iho, a i ʻole me nā lāʻau lapaʻau ʻē aʻe e like me ka chemotherapy.

Aia nā kumu like ʻole e hiki ai i kāu kauka ke ʻōlelo aku i ka lāʻau lapaʻau no ʻoe. Hiki ke hoʻohana ʻia e mālama a hoʻōla paha i kekahi mau lymphoma mua, a i ʻole e hoʻomaikaʻi i nā hōʻailona. Hiki ke loaʻa kekahi mau hōʻailona e like me ka ʻeha a i ʻole nāwaliwali inā ʻoi aku ka nui o kou maʻi lymphoma, a i ʻole ke kau ʻana i kou mau aʻalolo a i ʻole ke kuamoʻo. I kēia hihia, hāʻawi ʻia ka radiation e hōʻemi i ke koko a hoʻomaha i ke kaomi. Akā naʻe, ʻaʻole i manaʻo ʻia e hoʻohana ʻia i mea lapaʻau. 

Pehea e hana ai ka radiotherapy?

Hoʻopilikia ka X-ray i ka DNA o ka cell (ke genetic material o ke cell) i hiki ʻole ai i ka lymphoma ke hoʻoponopono iā ia iho. ʻO kēia ke kumu e make ai ke kelepona. He mau lā a he mau pule paha ma hope o ka hoʻomaka ʻana o ka mālama ʻana i ka radiation no ka make ʻana o nā cell. Hiki ke hoʻomau kēia hopena no kekahi mau mahina, no laila, ʻo nā mahina ma hope o kou hoʻopau ʻana i ka mālama ʻana, hiki ke hoʻopau ʻia nā cell lymphoma cancerous.

ʻO ka mea pōʻino, ʻaʻole hiki i ka radiation ke haʻi i ka ʻokoʻa ma waena o kāu mau maʻi maʻi a me nā mea maʻi ʻole. No laila, hiki iā ʻoe ke loaʻa i nā hopena ʻaoʻao e pili ana i kou ʻili a me kou kino kokoke i kahi āu e mālama ai i ka radiation. ʻO ka nui o nā ʻenehana radiation i kēia mau lā e ʻoi aku ka pololei o ka huli ʻana i ka maʻi kanesa, akā naʻe, no ka mea e pono ai ke hele ʻana o nā kukui X i kou ʻili a me nā ʻiʻo ʻē aʻe e hiki ai i ka lymphoma, hiki ke hoʻopilikia ʻia kēia mau wahi āpau.

Hiki i kāu kauka lapaʻau oncologist (ke kauka lapaʻau e hana ana me ka radiation) a i ʻole kahu hānai e hiki ke kamaʻilio me ʻoe e pili ana i nā hopena ʻaoʻao āu e loaʻa ai, ma muli o ka wahi o kou ʻōpū. Hiki iā lākou ke aʻo aku iā ʻoe i kekahi mau huahana ʻili maikaʻi e mālama ai i nā ʻeha ʻili āu e loaʻa ai.

Ua hoʻohana ʻia ka chemotherapy (chemo) e mālama i ka maʻi kanesa no nā makahiki he nui. Aia nā ʻano lāʻau chemo like ʻole a loaʻa paha iā ʻoe ma mua o hoʻokahi ʻano o ka chemotherapy e mālama ai i kāu CLL a i ʻole lymphoma. ʻO nā hopena ʻaoʻao āu e loaʻa ai e hilinaʻi ia i nā lāʻau lapaʻau chemotherapy āu e loaʻa ai. 

Pehea ka hana ʻana o ka chemo?

Hana ʻia ka Chemotherapy ma ka hoʻouka ʻana i nā cell e ulu wikiwiki ana. ʻO ia ke kumu e hana maikaʻi ai ia no nā lymphomas ikaika - a ulu wikiwiki paha. Eia nō naʻe, ʻo ia ka hana e kūʻē i nā cell ulu wikiwiki e hiki ke hoʻoulu i nā hopena ʻaoʻao i makemake ʻole ʻia i kekahi poʻe, e like me ka lauoho lauoho, nā ʻeha waha a me ka ʻeha (mucositis), nausea a me ka maʻi maʻi.

No ka mea hiki i ka chemo ke hoʻopili i kekahi cell e ulu wikiwiki ana, a ʻaʻole hiki ke haʻi i ka ʻokoʻa ma waena o nā sela olakino a me nā sela lymphoma cancerous - ua kapa ʻia ʻo ia he "systemic treatment", ʻo ia hoʻi, hiki ke hoʻopili ʻia kekahi ʻōnaehana o kou kino e nā hopena ʻaoʻao i hana ʻia e ka chemo.

Hoʻopiʻi nā chemotherapies like ʻole i ka lymphoma ma nā pae like ʻole o ka ulu ʻana. Ke hoʻouka nei kekahi mau mea maʻi maʻi maʻi maʻi maʻi maʻi maʻi e hoʻomaha ana, hoʻouka kekahi i nā mea e ulu hou ana, a hoʻouka kekahi i nā sela lymphoma nui loa. Ma ka hāʻawi ʻana i nā chemo's e hana ana i nā cell i nā pae like ʻole, aia ka hiki ke pepehi i nā mea lymphoma hou aʻe a loaʻa ka hopena maikaʻi aʻe. Ma ka hoʻohana ʻana i nā chemotherapies ʻē aʻe, hiki iā mākou ke hoʻohaʻahaʻa liʻiliʻi i nā doses ʻo ia hoʻi ka liʻiliʻi o nā hopena ʻaoʻao mai kēlā me kēia lāʻau lapaʻau, ʻoiai e loaʻa ana ka hopena maikaʻi loa.

Ua hoʻohana mua ʻia nā antibodies monoclonal (MAB) e mālama i ka lymphoma i ka hopena o nā makahiki 1990. Eia naʻe, i nā makahiki i hala iho nei, ua hoʻomohala ʻia nā antibodies monoclonal hou aʻe. Hiki iā lākou ke hana pololei e kūʻē i kāu lymphoma a i ʻole e huki i kāu mau pūnaewele ponoʻī i kāu mau sela lymphoma e hoʻouka a pepehi iā ia. Maʻalahi ka ʻike ʻana i nā MAB no ka mea ke hoʻohana ʻoe i ko lākou inoa maʻamau (ʻaʻole ko lākou inoa inoa), hoʻopau mau lākou me nā huaʻōlelo ʻekolu "mab". 

Pehea e hana ai nā antibodies monoclonal?

Hoʻohana wale nā ​​antibodies monoclonal i ka lymphoma inā loaʻa iā lākou nā protein kikoʻī ma luna o lākou. ʻAʻole loaʻa kēia mau hōʻailona lymphoma a pau, a hoʻokahi wale nō hōʻailona paha kekahi a ʻoi aku ka nui o kekahi. ʻO nā laʻana o nā protein i loaʻa ma nā pūnaewele lymphoma T-cell i hoʻopaʻa ʻia e kahi antibody monoclonal ʻo CD30 a me CCR4. 

Ke ulu nei kekahi mau pūniu lymphoma me kahi hōʻailona kikoʻī ma ke kelepona i loaʻa ʻole i kāu mau sela olakino. ʻO nā lāʻau lapaʻau i hoʻopaʻa ʻia he mau lāʻau e ʻike wale i kēlā māka kikoʻī, no laila hiki iā ia ke haʻi i ka ʻokoʻa ma waena o ka lymphoma a me nā cell olakino. 

Hoʻopili nā lāʻau lapaʻau i hoʻopaʻa ʻia i ka marker ma ka cell lymphoma a kāpae iā ia mai ka loaʻa ʻana o nā hōʻailona e ulu a palahalaha. ʻO kēia ka hopena i ka hiki ʻole i ka lymphoma ke loaʻa nā meaʻai a me ka ikehu e pono ai ke ulu, e hopena i ka make ʻana o ka cell lymphoma. 

Ma ka hoʻopili wale ʻana i nā hōʻailona ma nā pūnaewele lymphoma, hiki i ka lāʻau lapaʻau ke pale aku i ka hōʻino ʻana i kāu mau sela olakino. Loaʻa kēia i nā hopena ʻaoʻao liʻiliʻi ma mua o ka mālama ʻana i nā ʻōnaehana e like me chemo, ʻaʻole hiki ke haʻi i ka ʻokoʻa ma waena o ka lymphoma a me nā cell olakino. 

 

Nui nā lāʻau lapaʻau i hoʻopaʻa ʻia, kekahi mau chemotherapies a me nā immunotherapies e lawe ʻia e ka waha ma ke ʻano he papa a i ʻole capsule. ʻO nā lāʻau anti-cancer i lawe ʻia e ka waha i kapa ʻia ʻo "oral therapies". He mea nui e ʻike inā he lāʻau lapaʻau i hoʻopaʻa ʻia kāu lāʻau waha a i ʻole ka chemotherapy. Inā ʻaʻole maopopo ʻoe e nīnau i kāu kauka a kahu hānai paha. 

E ʻokoʻa nā hopena ʻaoʻao āu e nānā ai, a pehea ʻoe e hoʻokele ai iā lākou e like me ke ʻano o ka lāʻau lapaʻau waha āu e lawe nei.

 

He aha ke ʻano o ka hoʻololi ʻana i ka ʻōpū a i ʻole ka iwi iwi?

ʻO ka hoʻololi ʻana i ke kelepona he hana ia e hoʻohana ʻia e mālama i kāu lymphoma, a i ʻole e hoʻomau i ke kala ʻana no ka lōʻihi inā nui ka manawa e hoʻi hou ai kāu lymphoma (e hoʻi mai). Hiki nō hoʻi i kāu kauka ke ʻōlelo aku i kahi transplant cell stem no ʻoe ke hoʻi hou kāu lymphoma.

ʻO ka transplant cell stem kahi hana paʻakikī a invasive e hana ʻia i nā pae. Hoʻomākaukau mua ʻia nā poʻe maʻi e hoʻololi ana i ka stem cell me ka chemotherapy wale nō a i hui pū ʻia me ka radiotherapy. Hāʻawi ʻia ka lāʻau lapaʻau chemotherapy i hoʻohana ʻia i ka hoʻololi ʻana o ke kelepona stem ma nā ʻano kiʻekiʻe ma mua o ka maʻamau. ʻO ke koho o ka chemotherapy i hāʻawi ʻia i kēia kaʻina e pili ana i ke ʻano a me ka manaʻo o ka transplant. 

ʻIke hou aku e pili ana i nā Stem Cell Transplants

No ka ʻike hou aku e pili ana i ka transplant cell stem e ʻike i kā mākou ʻaoʻao pūnaewele.

Ka hoʻololi ʻana o nā pūnaʻi kumu - he hiʻohiʻona

ʻO ka hoʻololi ʻana o nā pūnaʻi pūʻali autologous - me ka hoʻohana ʻana i kāu mau pūnaewele ponoʻī

Ka hoʻololi ʻana o nā pūnaʻi kumu allogeneic – ka hoʻohana ʻana i nā pūnaewele kumu a kekahi mea ʻē aʻe

Hiki ke hoʻohana ʻia ke ʻokiʻoki e wehe i ka lymphoma holoʻokoʻa. Hiki ke hana ʻia kēia inā ʻoe hoʻokahi wahi kūloko o ka lymphoma hiki ke wehe maʻalahi. 

He ala koʻikoʻi nā hoʻokolohua lapaʻau e ʻimi ai i nā lāʻau lapaʻau hou, a i ʻole nā ​​hui pū ʻana o nā lāʻau lapaʻau e hoʻomaikaʻi i nā hopena no nā maʻi me ka lymphoma. Hiki iā lākou ke hāʻawi iā ʻoe i ka manawa e hoʻāʻo ai i nā ʻano lāʻau lapaʻau hou ʻaʻole i ʻae ʻia ma mua no kāu ʻano lymphoma.

Ke hoʻāʻo ʻia nei kekahi mau lāʻau lapaʻau i nā hoʻokolohua lapaʻau no nā lymphoma T-cell like ʻole e hiki iā ʻoe ke nīnau i kāu kauka e pili ana:

  • Azaciditidine (antimetabolite - Pyrimidine Nucleoside Analogue)
  • Anti CD-7 allogeneic CAR T-cell (gene/cellular therapy)
  • ʻO Valemetostat Tosylate (mea hoʻopale o EZH1 a me EZH2)
  •  AZD4573 (hoʻopaʻa CDK)
  • DR-01 (anti-CD94 antibody)
  • AZD4205 (JAK mea hoʻopaneʻe)
  • Anti-CD70 Allogeneic CRISPR-Cas9 (Nā Pūnaewele T i hana ʻia)
  • PTX-100 (GGTI-2418) – (Geranylgeranyltransferase I Inhibitor)
  •  CX-5461 (DNA RNA synthesis inhibitor)
  • ʻO Venetoclax (mea hoʻopaneʻe BCL2)

No ka ʻike hou aku e pili ana i nā hoʻokolohua lapaʻau, e kipa i kā mākou ʻaoʻao pūnaewele ma Ka hoʻomaopopo ʻana i nā hoʻokolohua Clinical ma ke kaomi ʻana ma aneʻi.

No ka ʻike hou aku
E nānā i nā lāʻau lapaʻau no Lymphoma
No kaʻike hou aku
Nā hopena ʻaoʻao o ka lāʻau lapaʻau

Ka wānana o ka T-cell lymphoma

ʻO ka wānana ka maikaʻi o ka pane ʻana i ka mālama ʻana no ka lymphoma a me ka hopena e hiki mai ana.

He nui ka poʻe e pane maikaʻi i nā lāʻau lapaʻau a hele i ke kala ʻana, ʻoiai inā loaʻa iā ʻoe kahi pane maikaʻi i ka wā mua, hoʻihoʻi pinepine ka T-cell lymphomas a pono e mālama ʻia ma mua o hoʻokahi manawa. 

ʻAʻole hiki i kekahi poʻe ke pane i ka lāʻau lapaʻau mua a pono lākou e hoʻāʻo i nā ʻano lāʻau like ʻole e loaʻa ai ka lymphoma i lalo. ʻO ka lymphoma i pane ʻole i ka lāʻau i kapa ʻia he refractory.

He mea kūʻokoʻa loa kāu wānana pilikino a hilinaʻi ʻia i kekahi mau kumu e like me: 

  • ka subtype o T-cell lymphoma iā ʻoe a me kona pae
  • kou mau makahiki a me kou olakino holoʻokoʻa
  • nā kumu genetic e pili ana i ka lāʻau lapaʻau
  • pehea ka pane maikaʻi o kou kino i ka lāʻau.
Aia kekahi mau kumu ʻē aʻe e pili ana i kāu wānana. E nīnau i kāu kauka e pili ana i kāu prognosis a me ka mea e manaʻo ai mai ka mālama ʻana.

Pahu o ka lapaau

ʻO ka pahuhopu o ka lāʻau lapaʻau ke komo i kahi hoʻōla, kala piha a hapa paha. He mea nui ka loaʻa ʻana o nā manaʻolana e pili ana i kāu mālama ʻana i hiki iā ʻoe ke hoʻolālā i kāu mea e pono ai. 

hoolaia

E kaomi ma luna o ke kāleka no ka ʻike hou aku
No ka ho'ōla 'ana mai ka lymphoma, 'o ia ho'i ma hope o ka mālama 'ana, 'a'ohe ou hō'ailona a hō'ailona paha o ka ma'i. Ua hala ka lymphoma mau loa - ʻaʻole ia e hoʻi mai.

Kala piha

E kaomi ma luna o ke kāleka e aʻo hou aku
Kāhea ʻia ka pane piha, me he lāʻau lāʻau lā. ʻAʻohe lymphoma i koe i loko o kou kino. Akā aia kekahi manawa e hoʻi mai (relapse) i kekahi lā. He mau mahina a mau makahiki paha kēia e hiki mai ana. ʻO ka lōʻihi o kou kala ʻana, ʻoi aku ka liʻiliʻi o ka hoʻi hou ʻana.

Kala kala ʻāpana

E kaomi ma luna o ke kāleka no ka ʻike hou aku
Kāhea ʻia he pane hapa. Loaʻa iā ʻoe ka lymphoma a i ʻole CLL, akā ʻoi aku ka liʻiliʻi ma mua o ka mālama ʻana. ʻAʻole hiki ke ho'ōla ʻia nā lymphoma a pau, no laila he hopena maikaʻi loa ka pane hapa. Hiki iā ia ke kōkua i ka hoʻomaikaʻi ʻana i kou maikaʻi o ke ola ma ka hōʻemi ʻana i nā hōʻailona.

Nā ʻano o ka T-cell Lymphoma

Hiki ke lohi ka ulu ʻana o nā lymphomas T-cell (ʻalolent) a i ʻole ka ulu wikiwiki ʻana (koʻikoʻi). ʻO ka hapa nui o nā lymphoma T-cell he mea ʻino. Kaomi ma nā kiko kiko ma lalo e aʻo e pili ana i nā ʻano ʻano like ʻole.

hōʻuluʻulu manaʻo

  • Hoʻoulu ʻia nā lymphomas T-cell i ka wā e loli ai nā lymphocytes T-cell a lilo i maʻi kanesa.
  • ʻO nā lymphocytes T-cell (T-cells) he ʻāpana koʻikoʻi o kāu ʻōnaehana pale, hoʻoponopono i nā pane kūlohelohe, hakakā ʻana i ka maʻi a me nā maʻi, a me ke kōkua ʻana i nā mea pale ʻē aʻe e hana maikaʻi.
  • ʻOiai ʻo T-cell kekahi ʻano o ke koko keʻokeʻo keʻokeʻo, ʻaʻole lākou e noho maʻamau i kou koko e like me nā ʻāpana koko ʻē aʻe.
  • Hana ʻia nā cell T i loko o kou iwi iwi a laila hele i kou thymus kahi e hoʻomau ai kou ulu a ulu. A laila, noho lākou i loko o kou thymus a me nā lymph nodes akā hiki ke hele i kekahi wahi o kou kino.
  • Aia ma kahi o 20 mau ʻano ʻano like ʻole o T-cell lymphoma a he kakaikahi loa kēlā me kēia.
  • Hiki i nā hōʻailona hōʻailona lymphoma maʻamau a pili paha i ka ʻāpana o kou kino kahi e ulu ai ka lymphoma.
  • He mea maʻamau nā hōʻailona B i kekahi mau lymphoma T-cell. E hōʻike i kāu kauka inā loaʻa iā ʻoe kēia mau hōʻailona.
  • Aia nā ʻano lapaʻau like ʻole no ka T-cell lymphoma a ʻo ka mālama ʻana iā ʻoe e hilinaʻi ʻia ma kāu ʻano subtype, makahiki a me kou olakino holoʻokoʻa, nā hōʻailona a me kāu mau makemake pilikino.
  • Hiki i nā lymphoma T-cell ke pane maikaʻi i ka lāʻau lapaʻau, akā hoʻi pinepine. Pono paha ʻoe e mālama i nā manawa he nui.
  • ʻAʻole ʻoe wale nō a hiki ke hoʻopili i kā mākou Lymphoma Care Nurses ma ke kaomi ʻana i ka Kāhea iā mā˚ou pihi ma ka lalo o ka papa.

Kākoʻo a me ka ʻike

E aʻo hou e pili ana i kāu hoʻāʻo koko ma aneʻi - Nā hoʻokolohua Lab ma ka pūnaewele

E aʻo hou e pili ana i kāu mau lapaʻau ma aneʻi - nā lāʻau anticancer eviQ - Lymphoma

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E ʻoluʻolu: Hiki i nā limahana Lymphoma Australia ke pane i nā leka uila i hoʻouna ʻia ma ka ʻōlelo Pelekania.

No ka poʻe e noho ana ma Australia, hiki iā mākou ke hāʻawi i ka lawelawe unuhi kelepona. E kāhea mai kāu kahu hānai a i ʻole ka ʻohana ʻōlelo Pelekania iā mākou e hoʻonohonoho i kēia.